ABSTRACT Sturge-Weber Syndrome is a rare, non-hereditary developmental condition characterized by hamartomatous vascular proliferations affecting the brain and facial tissues. Its main features include corticocerebral angiomatosis, cerebral calcifications, epilepsy, ocular abnormalities, mental impairment, and a facial port-wine stain. This report aims to highlight the main features of Sturge-Weber Syndrome in a patient with unilateral facial and scalp nevus, ipsilateral glaucoma, and imaging alterations. A case study was conducted on a patient treated at an ophthalmology clinic. The diagnosis and follow-up […]

The Sturge-Weber syndrome (SWS) is a rare congenital neuro-oculocutaneous disorder. This phacomatosis, also known as encephalotrigeminal angiomatosis, is defined by the classic triad: cutaneous, meningeal and ocular hemangiomas. Despite its typical presentation, incomplete forms are not uncommon. Glaucoma is often present and their pathophysiological mechanisms remain uncertain. Pherhaps this is why the clinical and surgical management of glaucoma associated with Sturge-Weber syndrome (GSSW) is a challenge for the ophthalmic practice, often with disappointing results. We present a literature review with […]

The authors describe a rare case of retinal racemose hemangiomatosis. We discuss the symptoms,the treatments, the evolution of this disease.