ABSTRACT Duane Syndrome (DS) is a rare ocular disorder that causes congenital strabismus. It results from a failure of the abducens nerve (VI cranial nerve) to innervate the lateral rectus muscle, in addition to anomalous innervation of this muscle by the oculomotor nerve (III cranial nerve). The syndrome is characterized by restricted movements of adduction and abduction, narrowing of the palpebral fissure, abnormal ocular movements, and globe retraction. It affects about 0.1% of the population and accounts for 1-4% of […]

The author presents his arguments to state that the Duane’s syndrome type III of the Huber’s classification does not exist. He takes the chance of those arguments to show why the medial rectus muscle recession in Duane’s syndrome with esotropia cripples the adduction more that it does in esotropias of other origins. He shows also why one must recess also the sound eye’s medial rectus in Duane’s syndrome with esotropia.

This article reports a case of a female five years old child with rare syndrome of Wilderwanck wich consists in a association of KlippelFeil syndrome and Duane syndrome and auditive hypoacusia. Ocular examination reveals alterations of cervical column, bilateral abduction limitations, aduction limitation of right eye associated with enophthalmos, palpebral fissure decrease, anisotropia in A, lateroversions esotropia and bilateral neurosensorial auditive hypoacusia. Our patient reveal an association of Klippel-Feil Syndrome type II with bilateral Duane Syndrome.