Objective: To evaluate in which phase of Vogt-Koyanagi-Harada (VKH) syndrome the patients receive the first attendance in specialized service. Methods: A retrospective study was conduted to evaluate medical records of 14 patients with VKH in the Clementino Fraga Filho University Hospital of the Federal University of Rio de Janeiro from January 2014 to March 2017. In this analysis, gender, age, stage of disease and visual acuity of these patients with at least probable VKH were recorded. Results: Of these patients, […]

Pellucid marginal degeneration (PMD) treatment can be challenging in moderate to advanced cases and penetrating keratoplasty should be avoided due to high risk of complications, such as graft rejection. We report a case of a 30-year-old female patient with PMD that was referred to our service with bilateral low visual acuity, worse in her right eye and contact lenses intolerance. We performed a corneal crescentic lamellar wedge resection that resulted in good useful vision and postponed the keratoplasty for eighteen […]

A degeneração marginal pelúcida (DMP) é uma ectasia corneana de difícil manejo em casos moderados e avançados. O transplante de córnea penetrante nesses pacientes deve ser evitado ao máximo tendo em vista que a descentração necessária do botão aumenta o risco de vascularização e consequentemente rejeição, além das dificuldades técnicas e possibilidade de deiscência de sutura devido ao afinamento corneano pronunciado característico desta ectasia. Nós relatamos o caso de uma paciente de 30 anos com DMP com queixa de baixa […]

The orbital pseudotumor is a benign idiopathic inflammatory disease. The authors present a case manifested in 12 years old boy, diagnosed by clinical, laboratory and radiological examination. There was a good response to treatment with corticosteroids proposed. The report is followed by brief literary resume on the subject.

In this paper we describe how we successfully conducted a case of neurotrophic ulcer not responsive to conventional therapy using scleral contact lens and the advantages of this therapy.

Female, 29, former smoker, diagnosed in September 2012 with Graves’ disease and rapid presentation of bilateral exophthalmos. In the ophthalmologic evaluation, it presented preserved motility, proptosis and upper fat sac in OA with retraction of PPSS and PPII and exophthalmetry in OD of 26 mm, and in OE of 24 mm. In May 2014, he performed the mapping of the retina that showed scars of chorioretinitis in both eyes and computerized campimetry, presenting a nasal step in OD, superior contraction, […]

The objective of the following work is to document the phenotypic expression variability in Best Disease in first-degree relatives. The information was collected by assessing medical notes, interviewing the patient and obtaining photographic record of the diagnostic methods to which the patient was submitted. Data was analyzed along with a thorough review of the literature. A series of cases were reported in which the patient presenting the phenotypic characteristics of the disease has first degree relatives without ophthalmic findings during […]

O objetivo do presente trabalho é a documentação da variabilidade de expressão fenotípica da Doença de Best em parentes de primeiro grau. As informações foram obtidas por meio de revisão do prontuário, entrevista com o paciente e registro fotográfico dos métodos diagnósticos aos quais os pacientes foram submetidos. Dados foram analisados junto a uma extensa revisão da literatura. Relatamos uma série de casos, no qual o paciente que apresenta as alterações fenotípicas da doença tem familiares de primeiro grau sem […]